Acylcarnitines, Plasma w/ Consultation




Test Mnemonic

ACYLBI

CPT Codes

  • 82017 - QTY (1)
  • 82379 - QTY (1)

Performing Laboratory

Cleveland Clinic Laboratories


Specimen Requirements

Volume Type Container Collect Temperature Transport Temperature Special Instructions
1 mLPlasmaEDTA (Lavender) FrozenRemove plasma from cells within 2 hours of collection and then freeze.

Alternate Specimen Requirements

Volume Type Container Collect Temperature Transport Temperature Special Instructions
1 mLPlasmaLithium heparin (Green) FrozenRemove plasma from cells within 2 hours of collection and then freeze.
1 mLPlasmaLithium heparin PST (Lt. Green) FrozenRemove plasma from cells within 2 hours of collection and then freeze.
1 mLSerumNo additive (Red) FrozenRemove serum from cells within 2 hours of collection and then freeze.
1 mLPlasmaSodium heparin (Green) FrozenRemove plasma from cells within 2 hours of collection and then freeze.

Minimum Specimen Requirements

Volume Type Container Collect Temperature Transport Temperature Special Instructions
0.2 mL     

Stability

Environmental Condition Description
FrozenAfter separation from cells: 60 days

Days Performed

1 day per week

Turnaround Time

1 - 10 days

Methodology

Name Description
High Performance Liquid Chromatography/Tandem Mass Spectrometry (LC/MS/MS) 

Reference Range

3-OH-Butyryl/IsoButyrylcarnitine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal2 - 84nmol/L
 30 Days364 DaysNormal6 - 114nmol/L
 1 Years99 YearsNormal3 - 40nmol/L
3-OH-Dodecanoylcarnitine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal1 - 5nmol/L
 30 Days364 DaysNormal1 - 7nmol/L
 1 Years99 YearsNormal1 - 7nmol/L
3-OH-Hexadecanoylcarnitine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal1 - 5nmol/L
 30 Days364 DaysNormal1 - 9nmol/L
 1 Years99 YearsNormal1 - 7nmol/L
3-OH-Hexadecenoylcarnitine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0 - 2nmol/L
 30 Days364 DaysNormal0 - 2nmol/L
 1 Years99 YearsNormal0 - 2nmol/L
3-OH-IsoValeryl/2-Methyl-3-OH-Butyrylcarnitine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal6 - 109nmol/L
 30 Days364 DaysNormal7 - 53nmol/L
 1 Years99 YearsNormal7 - 42nmol/L
3-OH-Linoleoylcarnitine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0 - 1nmol/L
 30 Days364 DaysNormal0 - 2nmol/L
 1 Years99 YearsNormal0 - 1nmol/L
3-OH-Oleoylcarnitine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0 - 2nmol/L
 30 Days364 DaysNormal0 - 3nmol/L
 1 Years99 YearsNormal0 - 2nmol/L
3-OH-Tetradecanoylcarnitine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal1 - 7nmol/L
 30 Days364 DaysNormal2 - 12nmol/L
 1 Years99 YearsNormal1 - 10nmol/L
3-OH-Tetradecenoylcarnitine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0 - 9nmol/L
 30 Days364 DaysNormal1 - 11nmol/L
 1 Years99 YearsNormal1 - 12nmol/L
Acetylcarnitine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal827 - 17279nmol/L
 30 Days364 DaysNormal589 - 24218nmol/L
 1 Years99 YearsNormal3571 - 17280nmol/L
Decanoylcarnitine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal14 - 178nmol/L
 30 Days364 DaysNormal17 - 202nmol/L
 1 Years99 YearsNormal12 - 251nmol/L
Decenoylcarnitine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal12 - 190nmol/L
 30 Days364 DaysNormal28 - 211nmol/L
 1 Years99 YearsNormal23 - 323nmol/L
Dodecanoylcarnitine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal12 - 132nmol/L
 30 Days364 DaysNormal9 - 196nmol/L
 1 Years99 YearsNormal9 - 114nmol/L
Dodecenoylcarnitine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal3 - 47nmol/L
 30 Days364 DaysNormal2 - 55nmol/L
 1 Years99 YearsNormal2 - 42nmol/L
Free L-carnitine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal7 - 54umol/L
 30 Days364 DaysNormal16 - 58umol/L
 1 Years99 YearsNormal22 - 52umol/L
Free/Total carnitine ratio
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0.6 - 0.9.
 30 Days364 DaysNormal0.4 - 0.9.
 1 Years99 YearsNormal0.7 - 0.9.
Glutarylcarnitine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal6 - 78nmol/L
 30 Days364 DaysNormal7 - 58nmol/L
 1 Years99 YearsNormal16 - 126nmol/L
Hexadecanoylcarnitine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal22 - 244nmol/L
 30 Days364 DaysNormal40 - 225nmol/L
 1 Years99 YearsNormal47 - 174nmol/L
Hexadecenoylcarnitine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal2 - 41nmol/L
 30 Days364 DaysNormal3 - 23nmol/L
 1 Years99 YearsNormal3 - 22nmol/L
Hexanoylcarnitine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal1 - 85nmol/L
 30 Days364 DaysNormal6 - 101nmol/L
 1 Years99 YearsNormal7 - 69nmol/L
Interpretation, Plasma Acylcarnitines
Sex Age From Age To Type Range Range Unit
       FreetextNormal 
Iso/Butyrylcarnitine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal19 - 239nmol/L
 30 Days364 DaysNormal14 - 266nmol/L
 1 Years99 YearsNormal50 - 364nmol/L
Isovaleryl/2-Methylbutyrylcarnitine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal8 - 462 nmol/L
 30 Days364 DaysNormal12 - 197nmol/L
 1 Years99 YearsNormal25 - 225nmol/L
Linoleoylcarnitine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal5 - 67nmol/L
 30 Days364 DaysNormal10 - 136nmol/L
 1 Years99 YearsNormal11 - 95nmol/L
Malonylcarnitine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal12 - 51nmol/L
 30 Days364 DaysNormal8 - 130nmol/L
 1 Years99 YearsNormal6 - 122nmol/L
Octanoylcarnitine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal14 - 176 nmol/L
 30 Days364 DaysNormal20 - 223nmol/L
 1 Years99 YearsNormal22 - 282nmol/L
OH-Dodecenoylcarnitine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0 - 8nmol/L
 30 Days364 DaysNormal0 - 3nmol/L
 1 Years99 YearsNormal0 - 3nmol/L
Oleoylcarnitine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal19 - 139nmol/L
 30 Days364 DaysNormal28 - 259nmol/L
 1 Years99 YearsNormal25 - 163nmol/L
Propionylcarnitine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal58 - 894nmol/L
 30 Days364 DaysNormal81 - 811nmol/L
 1 Years99 YearsNormal155 - 703nmol/L
Stearoylcarnitine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal10 - 66nmol/L
 30 Days364 DaysNormal15 - 107nmol/L
 1 Years99 YearsNormal19 - 65nmol/L
Succinylcarnitine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal10 - 128nmol/L
 30 Days364 DaysNormal8 - 108nmol/L
 1 Years99 YearsNormal15 - 59nmol/L
Tetradecadienoylcarnitine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal4 - 46nmol/L
 30 Days364 DaysNormal4 - 44nmol/L
 1 Years99 YearsNormal4 - 42nmol/L
Tetradecanoylcarnitine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal6 - 40nmol/L
 30 Days364 DaysNormal5 - 57nmol/L
 1 Years99 YearsNormal7 - 46nmol/L
Tetradecenoylcarnitine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal7 - 68nmol/L
 30 Days364 DaysNormal7 - 90nmol/L
 1 Years99 YearsNormal4 - 87nmol/L
Tiglylcarnitine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0 - 10nmol/L
 30 Days364 DaysNormal1 - 6nmol/L
 1 Years99 YearsNormal1 - 11nmol/L
Total L-carnitine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal12 - 68umol/L
 30 Days364 DaysNormal27 - 74umol/L
 1 Years99 YearsNormal27 - 66umol/L

Special Info

Decant plasma/serum from cells within 2 hours of collection. Indicate patient fasting hours when the specimen was collected. Fasting is not required, but the information is helpful for test interpretation. Carnitine, fish oil and omega-3 supplements affect test results; indicate supplement use on the requisition.