Mucopolysaccharides, Urine
Test Mnemonic
UMUCPO
CPT Codes
- 82664 - QTY (1)
- 83864 - QTY (1)
Aliases
- Glycosaminoglycans
Includes
- MPS Electrophoresis
- Mucopolysaccharides mg/mmol CRT
Performing Laboratory
ARUP
Specimen Requirements
| Volume | Type | Container | Collect Temperature | Transport Temperature | Special Instructions |
|---|---|---|---|---|---|
| 20 mL | Urine, random | Clean container | Frozen, Critical | Morning void preferred. Freeze specimen immediately. |
Minimum Specimen Requirements
| Volume | Type | Container | Collect Temperature | Transport Temperature | Special Instructions |
|---|---|---|---|---|---|
| 10 mL |
Stability
| Environmental Condition | Description |
|---|---|
| Ambient | Unacceptable |
| Refrigerated | Unacceptable |
| Frozen | 1 month (avoid repeated freeze/thaw cycles) |
Days Performed
Tue
Turnaround Time
5 - 15 days
Methodology
| Name | Description |
|---|---|
| Electrophoresis | |
| Spectrophotometry (S) |
Reference Range
| Mucopolysaccharides, Urine | |||||
|---|---|---|---|---|---|
| Sex | Age From | Age To | Type | Range | Range Unit |
| Months | 5 Months | Normal | 14.6 - 47.8 | mg/mmol CRT | 6 Months | 11 Months | Normal | 3.7 - 35.5 | mg/mmol CRT | 1 Years | 2 Years | Normal | 5.4 - 30.8 | mg/mmol CRT | 3 Years | 6 Years | Normal | 5.2 - 16.7 | mg/mmol CRT | 7 Years | 13 Years | Normal | 2.4 - 10.2 | mg/mmol CRT | 14 Years | 99 Years | Normal | 0.0 - 7.1 | mg/mmol CRT |
Special Info
Morning void preferred. This test is New York state approved.
Clinical Info
This test is used to evaluate symptomatic patients for mucopolysaccharidoses (MPS). Mucopolysaccharides (Glycosaminoglycans) include: Keratan Sulfate, Heparan Sulfate, Dermatan Sulfate, and Chondroitin Sulfates 4 and 6. The excretion of Heparan Sulfate is variable. A normal mucopolysaccharides screen does not exclude Sanfilippo Syndrome (Mucopolysaccharidosis Type III).