Organic Acids Ur, Quant w/ Consultation




Test Mnemonic

UORABI

CPT Codes

  • 83918 - QTY (1)

Performing Laboratory

Cleveland Clinic Laboratories


Specimen Requirements

Volume Type Container Collect Temperature Transport Temperature Special Instructions
10 mLUrine, randomClean container (No preservatives) FrozenPlace specimen on ice after collection.

Minimum Specimen Requirements

Volume Type Container Collect Temperature Transport Temperature Special Instructions
5 mL    Place specimen on ice after collection.

Stability

Environmental Condition Description
Ambient3 hours
Refrigerated24 hours
Frozen3 months

Days Performed

2 days per week

Methodology

Name Description
Gas Chromatography Mass Spectrometry (GCMS) 

Reference Range

2HydroxyButyrate, Ur
Sex Age From Age To Type Range Range Unit
 2 Days29 DaysNormal0.2 - 9.6umol/mmolCr
 30 Days364 DaysNormal0.0 - 15.0umol/mmolCr
 1 Years99 YearsNormal0.0 - 2.7umol/mmolCr
2HydroxyGlutaricAcid
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal3.0 - 49.1umol/mmolCr
 30 Days364 DaysNormal4.4 - 66.9umol/mmolCr
 1 Years99 YearsNormal0.6 - 17.7umol/mmolCr
2MEButyrylGlycine,Ur
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0.0 - 1.0umol/mmolCr
 30 Days364 DaysNormal0.0 - 0.9umol/mmolCr
 1 Years99 YearsNormal0.0 - 0.4umol/mmolCr
2OH-IsoValerate, Ur
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0.0 - 0.2umol/mmolCr
 30 Days364 DaysNormal0.0 - 0.1umol/mmolCr
 1 Years99 YearsNormal0.0 - 0.1umol/mmolCr
2-OxoAdipic Acid, Ur
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0.0 - 0.0umol/mmolCr
 30 Days364 DaysNormal0.0 - 2.8umol/mmolCr
 1 Years99 YearsNormal0.0 - 3.3umol/mmolCr
3HydroxyButyrate, Ur
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0.1 - 4.4umol/mmolCr
 30 Days364 DaysNormal0.4 - 9.9umol/mmolCr
 1 Years99 YearsNormal0.1 - 2.6umol/mmolCr
3HydroxyGlutaricAcid
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0.0 - 0.7umol/mmolCr
 30 Days364 DaysNormal0.0 - 2.5umol/mmolCr
 1 Years99 YearsNormal0.0 - 0.7umol/mmolCr
3-HydroxyIsoValerate
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0.0 - 72.4umol/mmolCr
 30 Days364 DaysNormal1.7 - 119.3umol/mmolCr
 1 Years99 YearsNormal2.1 - 27.3umol/mmolCr
3MECrotonylGlycine,U
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal<0.3umol/mmolCr
 30 Days364 DaysNormal<0.3umol/mmolCr
 1 Years99 YearsNormal<0.3umol/mmolCr
3-Methylglutaconate
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0.0 - 5.2umol/mmolCr
 30 Days364 DaysNormal0.0 - 7.9umol/mmolCr
 1 Years99 YearsNormal0.0 - 2.0umol/mmolCr
3MethylGlutarate, Ur
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0.0 - 0.9umol/mmolCr
 30 Days364 DaysNormal0.1 - 1.4umol/mmolCr
 1 Years99 YearsNormal0.0 - 0.6umol/mmolCr
3OH2MethButyrate, Ur
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0.0 - 0.8umol/mmolCr
 30 Days364 DaysNormal0.0 - 5.6umol/mmolCr
 1 Years99 YearsNormal0.0 - 1.3umol/mmolCr
4OHPhenylAcetate, Ur
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal3.1 - 146.6umol/mmolCr
 30 Days364 DaysNormal14.3 - 569.5umol/mmolCr
 1 Years99 YearsNormal5.7 - 147.5umol/mmolCr
4OHPhenylLactate, Ur
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0.4 - 112.6umol/mmolCr
 30 Days364 DaysNormal1.1 - 88.2umol/mmolCr
 1 Years99 YearsNormal1.3 - 23.0umol/mmolCr
5-Oxo-Proline, Urine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0.0 - 7.3umol/mmolCr
 30 Days364 DaysNormal0.0 - 7.8umol/mmolCr
 1 Years99 YearsNormal0.4 - 3.1umol/mmolCr
AcetoAcetate, Urine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0.0 - 0.1umol/mmolCr
 30 Days364 DaysNormal0.0 - 2.3umol/mmolCr
 1 Years99 YearsNormal0.0 - 0.5umol/mmolCr
Aconitate, Urine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal5.9 - 161.3umol/mmolCr
 30 Days364 DaysNormal26.3 - 330.8umol/mmolCr
 1 Years99 YearsNormal8.5 - 109.6umol/mmolCr
Adipic Acid, Urine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0.5 - 52.5umol/mmolCr
 30 Days364 DaysNormal5.0 - 53.8umol/mmolCr
 1 Years99 YearsNormal0.3 - 9.2umol/mmolCr
a-KetoGlutarate, Ur
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0.0 - 403.2umol/mmolCr
 30 Days364 DaysNormal0.2 - 355.8umol/mmolCr
 1 Years99 YearsNormal0.2 - 42.7umol/mmolCr
Benzoic Acid, Urine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0.0 - 9.6umol/mmolCr
 30 Days364 DaysNormal0.0 - 16.3umol/mmolCr
 1 Years99 YearsNormal0.0 - 14.6umol/mmolCr
ButyrylGlycine, Ur
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0.0 - 2.7umol/mmolCr
 30 Days364 DaysNormal0.0 - 2.7umol/mmolCr
 1 Years99 YearsNormal0.0 - 0.7umol/mmolCr
EthylMalonate, Urine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0.6 - 34.5umol/mmolCr
 30 Days364 DaysNormal0.7 - 82.7umol/mmolCr
 1 Years99 YearsNormal0.5 - 6.2umol/mmolCr
Fumarate, Urine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal1.0 - 26.4umol/mmolCr
 30 Days364 DaysNormal2.2 - 19.8umol/mmolCr
 1 Years99 YearsNormal0.3 - 2.6umol/mmolCr
Glutarate, Urine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0.0 - 6.2umol/mmolCr
 30 Days364 DaysNormal0.4 - 6.6umol/mmolCr
 1 Years99 YearsNormal0.0 - 1.4umol/mmolCr
HexanoylGlycine, Ur
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0.0 - 0.5umol/mmolCr
 30 Days364 DaysNormal0.0 - 0.3umol/mmolCr
 1 Years99 YearsNormal0.0 - 0.1umol/mmolCr
Interpretation, Urine Organic Acids
Sex Age From Age To Type Range Range Unit
       Normal 
IsoButyrylGlycine,U
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0.0 - 1.1umol/mmolCr
 30 Days364 DaysNormal0.0 - 1.1umol/mmolCr
 1 Years99 YearsNormal0.0 - 1.2umol/mmolCr
IsoCitric Acid, Urine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal2.4 - 297.4umol/mmolCr
 30 Days364 DaysNormal43.9 - 537.3umol/mmolCr
 1 Years99 YearsNormal9.1 - 271.9umol/mmolCr
Lactate, Urine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal35.5 - 282.4umol/mmolCr
 30 Days364 DaysNormal15.4 - 198.6umol/mmolCr
 1 Years99 YearsNormal2.9 - 47.2umol/mmolCr
Malate, Urine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0.4 - 12.8umol/mmolCr
 30 Days364 DaysNormal0.9 - 11.1umol/mmolCr
 1 Years99 YearsNormal0.0 - 1.1umol/mmolCr
Malonate, Urine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0.0 - 0.4umol/mmolCr
 30 Days364 DaysNormal0.0 - 0.4umol/mmolCr
 1 Years99 YearsNormal0.0 - 0.1umol/mmolCr
MethylCitrate, Urine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0.0 - 16.8umol/mmolCr
 30 Days364 DaysNormal1.7 - 25.4umol/mmolCr
 1 Years99 YearsNormal1.0 - 13.9umol/mmolCr
MethylMalonate, Urine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0.0 - 2.0umol/mmolCr
 30 Days364 DaysNormal0.0 - 2.2umol/mmolCr
 1 Years99 YearsNormal0.0 - 0.6umol/mmolCr
MethylSuccinate, Ur
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0.0 - 5.6umol/mmolCr
 30 Days364 DaysNormal0.1 - 6.8umol/mmolCr
 1 Years99 YearsNormal0.0 - 1.4umol/mmolCr
N-AcetylAsparticAcid
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0.2 - 40.0umol/mmolCr
 30 Days364 DaysNormal0.0 - 69.0umol/mmolCr
 1 Years99 YearsNormal0.1 - 8.9umol/mmolCr
N-AcetylTyrosine, Ur
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0.0 - 3.7umol/mmolCr
 30 Days364 DaysNormal0.0 - 4.9umol/mmolCr
 1 Years99 YearsNormal0.0 - 1.2umol/mmolCr
Oxalic Acid, Urine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal2.2 - 73.4umol/mmolCr
 30 Days364 DaysNormal6.9 - 76.4umol/mmolCr
 1 Years99 YearsNormal0.7 - 12.4umol/mmolCr
Pyruvate, Urine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0.4 - 5.7umol/mmolCr
 30 Days364 DaysNormal0.2 - 13.2umol/mmolCr
 1 Years99 YearsNormal0.1-2.6umol/mmolCr
Sebacic Acid, Urine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0.0 - 4.6umol/mmolCr
 30 Days364 DaysNormal0.0 - 12.4umol/mmolCr
 1 Years99 YearsNormal0.0 - 0.3umol/mmolCr
Suberic Acid, Urine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0.0 - 23.1umol/mmolCr
 30 Days364 DaysNormal2.4 - 30.7umol/mmolCr
 1 Years99 YearsNormal0.0 - 7.4umol/mmolCr
SuberylGlycine, Ur
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0.0umol/mmolCr
 30 Days364 DaysNormal0.0umol/mmolCr
 1 Years99 YearsNormal0.0umol/mmolCr
Succinate, Urine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal1.1 - 219.5umol/mmolCr
 30 Days364 DaysNormal7.7 - 189.6umol/mmolCr
 1 Years99 YearsNormal0.3 - 27.4umol/mmolCr
SuccinylAcetone, Ur
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal<0.4umol/mmolCr
 30 Days364 DaysNormal<0.4umol/mmolCr
 1 Years99 YearsNormal<0.4umol/mmolCr
Uracil, Urine
Sex Age From Age To Type Range Range Unit
   Days29 DaysNormal0.0 - 1.6umol/mmolCr
 30 Days364 DaysNormal0.0 - 7.7umol/mmolCr
 1 Years99 YearsNormal0.0 - 5.1umol/mmolCr
Urine, Creatinine
Sex Age From Age To Type Range Range Unit
Male18 Years99 YearsNormal46.8-314.5mg/dL
Female18 Years99 YearsNormal42.2-237.9mg/dL

Special Info

Order code UORABI is for urine organic acid analysis on patients of any age.